Dentin Dysplasia Type II

Definition: Genetic disorder affecting dentin formation, characterized by coronal dentin abnormalities. Less common than dentinogenesis imperfecta.

Radiographic Features:

• Location: Affects dentin and pulp chamber/root canal space of all teeth
• Edge: Well-defined
• Shape:
  • Pulp chamber may have ‘thistle’ or ‘flame’ shape
  • Progressive obliteration of pulp chamber and root canal space post-eruption
• Internal structure:
  • Radiopaque, similar to normal dentin
  • Absent or small pulp chamber and root canals
• Other: Possible presence of pulp stones

Key points:

• Genetic basis: Autosomal-dominant abnormality of DSPP gene
• Two types:
  1. Type I: Radicular (root) changes
  2. Type II: Coronal (crown) changes
• Affects all teeth in the dentition

Clinical significance:

• May lead to early tooth wear or fracture
• Potential for periapical infections due to pulp obliteration
• Challenges in endodontic treatment due to reduced pulp space
• May require prosthodontic intervention for aesthetics and function

Note: Differentiate from dentinogenesis imperfecta, which has similar radiographic features but different genetic basis and clinical presentation.