Dentinogenesis Imperfecta

Definition: Hereditary disorder affecting dentin formation, resulting in altered dentin morphology and structure.

Radiographic Features:

• Location: Affects dentin of all teeth
• Edge: Well-defined
• Shape:
  • Crowns: Bulbous
  • Roots: Short and slender
• Internal structure:
  • Radiopaque, similar to normal dentin
  • Absent or small pulp chamber and root canals
• Number: Affects all teeth in the dentition

Key points:

• Three types:
  1. Type I: Associated with osteogenesis imperfecta
  2. Type II: Isolated form
  3. Type III: Rare variant
• Teeth appear bluish-gray clinically

Clinical significance:

• Increased susceptibility to wear, fracture, and attrition
• May require full-coverage restorations for protection and aesthetics
• Challenges in endodontic treatment due to obliterated pulp spaces
• Early diagnosis crucial for preventive care and treatment planning

Note: Differentiate from dentin dysplasia, which has similar radiographic features but different genetic basis and clinical presentation.